En construction
Andersen–Tawil syndrome (ATS) is a rare arrhythmia disorder combining a signature arrhythmia phenotype, consisting of a pronounced U-wave and frequent ventricular extrasystoles (Figure 1) with extracardiac features including periodic paralysis and dysmorphic features. Occasionally, complex ventricular arrhythmias including bidirectional ventricular tachycardia and ventricular fibrillation occur.
The pronounced U-wave can easily be distinguished from the ST segment, and the QT interval itself is actually not prolonged
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